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USMLE Brs Pathology Vocab

Subjects : health-sciences, usmle
Instructions:
  • Answer 50 questions in 15 minutes.
  • If you are not ready to take this test, you can study here.
  • Match each statement with the correct term.
  • Don't refresh. All questions and answers are randomly picked and ordered every time you load a test.

This is a study tool. The 3 wrong answers for each question are randomly chosen from answers to other questions. So, you might find at times the answers obvious, but you will see it re-enforces your understanding as you take the test each time.
1. Sphingomyelin containing phagocytes seen in Niemman::Pick dx in liver - spleen - lymph nodes and skin






2. Aka lentigo maligna - precursor to lentigo maligna melanoma






3. Severe unconj hyperbilirubinemia due to deficient glucuronyl transferase






4. Aka chronic progressive histiocytosis - not as bad as Letterer Siwe






5. Associated with Wegener granulomatosis






6. Clear cell renal tumor seen in kids






7. Radiologic appearance of periostium in bone tumors






8. Aka infantile progressive spinal muscular atrophy - autosomal recessive - LMN disease - infants






9. Dysplastic cell seen in HPV






10. Autosomal recessive - neutropenia - albinism - cranial and peripheral neuropathy - tendency to develop repeated infections - abnormal WBCs (abnormal mictotubul formation and large cytoplasmic granules = lysosomes)






11. Pigmented iris hamartoma seen in neurofibromatosis






12. Polyostotic fibrous dysplasia - precocious puberty - caf






13. Osteophytes at PIP joints






14. Mucopolysaccharidosis - deficient a L iduronidase - accumulations of heparin sulfate and dermatan sulfate in heart - brain - liver - and other organs - progressive - hepatosplenomagaly - dwarfism - gargoyle - like facies - stubby fingers - corneal cl






15. Development of large pituitary adenomas following bilat adrenalectomy






16. Deficient hexosaminidase A - GM2 ganglioside accumulation - especially in neurons - CNS degeneration - mental/motor deterioration - blindness - cherry red spot on macula - death by 4 years of age






17. Deficient glucose -6- phosphatase - accumulation of glycogen in liver and kidney - hepatomegaly - hypoglycemia






18. Mucinous cell - characteristic of stomach CA met to ovary (krukenberg tumor)






19. Similar to paget breast - sometimes related to underlying adenoCA of sweat glands






20. Autosomal dominant - fatal - progressive degeneration of striatum and frontal cortex with neuronal depletion and gliosis






21. Occurs in SLE - small vegitations on either or both surfaces of valves






22. Diffuse nodular diabetic glomerulosclerosis






23. Peripheral neuropathy - atrophy of muscles - wet - high output cardiac failure - DCM - AV shunting - hypervolemia






24. Seen in urine of patients with multiple myeloma - Ig light chain either k or l






25. Small round blue cell tumor of bone - long bones - kids - 11:22 transloc






26. Aka congenital megacolon - dilation of colon due to absence of ganglion cells






27. Paraneoplastic synd looks like myasthenia gravis - often small cell lung CA






28. Aka pituitary cachexia - generalized panhypopituitarism






29. Small follicles filled with eosinophilic secretion - diagnostic feature of granulose cell tumor






30. Seen in hyperacute rejection - = acute inflammation - fibrinoid necrosis of small vessels - and extensive thrombosis






31. Infectious disorder - caused postencephalitic parkinsonism






32. Superclavicular lymph node identifying metastatic stomach CA






33. Aka mucocutaneous lymph node syndrome - acute self - limited - infants and young kids - acute necrotizing vasculitis of small and medium vessels - fever hemorrhagic edema of conjunctivae - lips and oral mucosa - and cervical LAD - can cause coronary






34. Thiamine deficiency - cerebral dysfunction - aka alcoholic encephalopathy - hemorrhagic lesions in the mamillary bodies - confusion - ataxia - ophthalmoplegia - and memory loss plus confabulation p 105 and p115






35. Aggressive B- cell lymphoma - EBV - starry sky appearance - c myc






36. Seen in insulinoma - episodic hyperinsulinemia and hypoglycemia - CNS dysfunction - reversal of CNS probs with administration of glucose






37. Different in that it is the primary disorder - recurrent vasospasm of small arteries and venules - pallor - cyanosis - fingers and toes - young healthy women






38. Appears as multiple wart - like lesions resembling condyloma accuminatum






39. Variant of rheumatoid arthritis - aka juvenile rheumatoid arthritis






40. Gene product inhibits apoptosis






41. Defective cilia - sinusitis - bronchiectasis - situs inversus - sometimes hearing loss and male sterility






42. Osteophytes at DIP joints






43. Non::neoplastic tumor like masses - fibrous replacement of resorbed bone






44. Transloc seen in ewing sarcoma






45. Intracytoplasmic proximal dentritic eosinophilic inclusions consisting of actin seen in Alzheimers






46. Combination of hyperthyroidism - nodular goiter - absence of exophthalmos






47. Malabsorption syndrome - Tropheryma wippelii bacilli - small intestine commonly affected - arthralgias - cardiac - and neuro symptoms






48. Follicular lymphoma IG heavy chain on 14 - bcl -2 oncogene on 18






49. Port wine stain on face - ipsilateral glaucoma - vascular lesions of ocular choroidal tissue - extensive hemangiomatous involvement of meninges






50. Deficient debranching enzyme amylo -1 -6- glucosidase - glycogen in liver - heart - skeletal muscle - stunted growth - hepatomegaly - hypoglycemia