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USMLE Brs Pathology Vocab

Subjects : health-sciences, usmle
Instructions:
  • Answer 50 questions in 15 minutes.
  • If you are not ready to take this test, you can study here.
  • Match each statement with the correct term.
  • Don't refresh. All questions and answers are randomly picked and ordered every time you load a test.

This is a study tool. The 3 wrong answers for each question are randomly chosen from answers to other questions. So, you might find at times the answers obvious, but you will see it re-enforces your understanding as you take the test each time.
1. Hemorrhagic urticaria of extensor surgaces of arms - legs - and buttocks - with fever - arthralgias - and GI renal involvement similar to IgA nephropathy - associated with URIs






2. Hemihypertrophy - macroglossia - organomegaly - neonatal hypoglycemia - various embryonal tumors - deleted WT 2 gene






3. Defective cilia - sinusitis - bronchiectasis - situs inversus - sometimes hearing loss and male sterility






4. Autoimmune hypothyroid - hurthle cells common






5. Mutation here causes pseudohypoparathyroidism






6. Mutation = paroxysmal nocturnal hemoglobinuria






7. Small follicles filled with eosinophilic secretion - diagnostic feature of granulose cell tumor






8. Aka congenital megacolon - dilation of colon due to absence of ganglion cells






9. Located on xsome 6 - mutation here = hereditary hemochromatosis






10. Deficient glucose -6- phosphatase - accumulation of glycogen in liver and kidney - hepatomegaly - hypoglycemia






11. Myc :: neuroblastoma amplicatiion correlates inversely with degree of differentiation






12. Development of large pituitary adenomas following bilat adrenalectomy






13. Transloc seen in ewing sarcoma






14. At least 2 X and one Y - hypogonadism - tall - gynecomastia - low testosterone - high pituitary gonadotropins - infertility -






15. Autosomal dominant - numerous adenomatous polyps along with osteomas and soft tissue tumors






16. Deficient a1 -4 glucosidase - accumulation of glycogen in liver - heart - skeletal muscle - cardiomegaly - muscle hypotonia - spelnomegaly - intractable hypoglycemia - death from cardiorespiratory failure before age 3






17. Nuclei arranged in horseshoe - shaped pattern about periphery of cell - characteristic of but not specific for granulomatous TB (as opposed to a foreign body giant cell that has scattered nuclei)






18. Tumor suppressor mutated in Von Recklinhousen






19. Aka acute disseminated langerhans cell histiocytosis - aggressive - usually fatal - kids hepatosplenomegaly - LAD - pancytopenia - pulmonary involvement - recurrent infections






20. Iron deficient anemia associated with upper::esophageal web






21. Deficient fibrillin (constituent of microfibrils) - arachnodactyly - ectopia lentis - aortic aneurysm - mitral valve prolapsed






22. Abnormal WT 1 gene - intersexual disorders - nephropathy - wilms tumor






23. Epithelial cells with eosinophilc granular cytoplasm seen in hashimoto






24. Vaginal epithelial cell with stippled appearance due to adherent coccobacilli






25. Catastrophic adrenal insuff and vascular collapse - hemorrhagic necrosis of adrenal cortex






26. Aka trisomy 13 - mental retardation - microcephaly - micropthalmia - brain abnormalities - cleft lip/palate - polydactyly - rockerbottom feet - congenital heart dx






27. Deficient muscle phosphorylase - glycogen in skeletal muscle - cramps with exertion






28. Osteophytes at DIP joints






29. Aka osteopetrosis - marble bone dx - dense skeleton - failure of osteoclastic activity






30. Seen in Down synd - small white spots on periphery of iris






31. Associated with breast alone (isn't one of these associated with prostate? Check)






32. Clear cell renal tumor seen in kids






33. Diffuse nodular diabetic glomerulosclerosis






34. Small round eosinophilic masses found in dieing hepatocytes often containing chromatin remnants seen in viral hepatitis






35. Paraneoplastic synd looks like myasthenia gravis - often small cell lung CA






36. Adenomatous polyps with tumors of CNS






37. Intracytoplasmic inclusions seen in leydig cell tumors p283






38. Pigmented iris hamartoma seen in neurofibromatosis






39. Single erythematous plaque on shaft of penis or scrotum






40. B1 thiamine - B2 riboflavin - B3 niacin - B6 pyridoxine - B12 cobalamin - C ascorbic acid - D calciferol - E a::tocopherol






41. Retinoblastoma on chromosome 13






42. Occurs in SLE - small vegitations on either or both surfaces of valves






43. Ovarian tumor resembling bladder transitional epith






44. Infectious disorder - caused postencephalitic parkinsonism






45. = MEN1






46. Downward displacement of cerebellar tonsils and medulla through foramen magnum






47. Tennis racket shaped cytoplasmic inclusion seen in langerhans cells (so also seen in langerhan cell histiocytosis)






48. Deficient debranching enzyme amylo -1 -6- glucosidase - glycogen in liver - heart - skeletal muscle - stunted growth - hepatomegaly - hypoglycemia






49. Osteophytes at PIP joints






50. Peripheral neuropathy - atrophy of muscles - wet - high output cardiac failure - DCM - AV shunting - hypervolemia