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USMLE Brs Pathology Vocab

Subjects : health-sciences, usmle
Instructions:
  • Answer 50 questions in 15 minutes.
  • If you are not ready to take this test, you can study here.
  • Match each statement with the correct term.
  • Don't refresh. All questions and answers are randomly picked and ordered every time you load a test.

This is a study tool. The 3 wrong answers for each question are randomly chosen from answers to other questions. So, you might find at times the answers obvious, but you will see it re-enforces your understanding as you take the test each time.
1. X linked - aka immunodeficiency with thrombocytopenia and eczema - total immunoglobulins often normal - recurrent infections






2. Intracytoplasmic proximal dentritic eosinophilic inclusions consisting of actin seen in Alzheimers






3. Development of large pituitary adenomas following bilat adrenalectomy






4. Hemorrhagic urticaria of extensor surgaces of arms - legs - and buttocks - with fever - arthralgias - and GI renal involvement similar to IgA nephropathy - associated with URIs






5. Diffuse nodular diabetic glomerulosclerosis






6. Manifestation of lymphplasmocytic lymphoma - B cell neoplasm






7. Deficient a1 -4 glucosidase - accumulation of glycogen in liver - heart - skeletal muscle - cardiomegaly - muscle hypotonia - spelnomegaly - intractable hypoglycemia - death from cardiorespiratory failure before age 3






8. Protooncogene mutated in medulary thyroid CA (MENII)






9. Severe unconj hyperbilirubinemia due to deficient glucuronyl transferase






10. Also seen in urine of MM - stacks of RBCs - will have high ESR






11. Hemihypertrophy - macroglossia - organomegaly - neonatal hypoglycemia - various embryonal tumors - deleted WT 2 gene






12. Malabsorption syndrome - Tropheryma wippelii bacilli - small intestine commonly affected - arthralgias - cardiac - and neuro symptoms






13. Different in that it is the primary disorder - recurrent vasospasm of small arteries and venules - pallor - cyanosis - fingers and toes - young healthy women






14. Follicular lymphoma IG heavy chain on 14 - bcl -2 oncogene on 18






15. Oligohydramnios causes fetus to be smashed






16. Autosomal dominant - numerous adenomatous polyps along with osteomas and soft tissue tumors






17. Dysplastic cell seen in HPV






18. Nystagmus - intention tremor - scanning speech - seen in MS






19. Similar to Hurler - deficient L iduronosulfate sulfatase - accumulations of heparin sulfate and dermatan sulfate - hepatospenomegaly - micrognathia - retinal degeneration - joint stiffness - mental retardation - cardiac lesions






20. X linked - absence of plasma cells and serum immunoglobulins - cell mediated immunity still ok - no germinal centers - recurrent bacterial infections - resistances to fungal and viral still - btk gene defect






21. Aka acute disseminated langerhans cell histiocytosis - aggressive - usually fatal - kids hepatosplenomegaly - LAD - pancytopenia - pulmonary involvement - recurrent infections






22. Thiamine deficiency - cerebral dysfunction - aka alcoholic encephalopathy - hemorrhagic lesions in the mamillary bodies - confusion - ataxia - ophthalmoplegia - and memory loss plus confabulation p 105 and p115






23. Hemangioblastoma or cavernous hemangioma of cerebellum - brainstem or retina - adenomas - cysts in liver - kidney - pancreas - and other organs - increased renal cell CA - gene = short arm of chromosome 3






24. B1 thiamine - B2 riboflavin - B3 niacin - B6 pyridoxine - B12 cobalamin - C ascorbic acid - D calciferol - E a::tocopherol






25. Autoimmune hypothyroid - hurthle cells common






26. Deficient fibrillin (constituent of microfibrils) - arachnodactyly - ectopia lentis - aortic aneurysm - mitral valve prolapsed






27. Peripheral neuropathy - atrophy of muscles - wet - high output cardiac failure - DCM - AV shunting - hypervolemia






28. Aka congenital megacolon - dilation of colon due to absence of ganglion cells






29. Aka trisomy 18 - mental retardation - prominent occiput - micrognathia (small jaw) - low::set ears - rocker::bottom feet - finger deformities - congenital heart dx






30. Primary adrenal failure






31. Small follicles filled with eosinophilic secretion - diagnostic feature of granulose cell tumor






32. Eosinophilic intracytoplasmic inclusions in hippocampus and purkinje cells seen in rabies infection






33. Parkinsonism with autonomic dysfunction and orthostatic hypotension






34. Aka trisomy 13 - mental retardation - microcephaly - micropthalmia - brain abnormalities - cleft lip/palate - polydactyly - rockerbottom feet - congenital heart dx






35. Autosomal recessive - conj hyperbilirubinemia - defect in bili transport - black color to liver






36. Iron deficient anemia associated with upper::esophageal web






37. Thyroid replacement by fibrous tissue - unkown origin - mimics






38. B Thalassemia major






39. Materal transmission del(15)(q11q13) - aka happy puppet syndrome - mental retardation - ataxia - seizures - inappropriate laughter






40. Eczematoid lesion of nipple areola - large cells with clear 'halo like' area - invade epidermis - underlying ductal CA






41. Defective in x- linked brutons agammaglobulinemia - B- cell tyrosine kinase






42. Associated with 90% cases of ankylosing spondylitis - common in rheumatoid arthritis






43. Tumor suppressor common in familial polyposis coli and adenoCA of colon as well as other tumors






44. Triad of ovarian fibroma - ascites - hydrothorax






45. Acute promyelocytic leukemia PML gene on 15 and RARa on 17






46. Paternal transmission del (15)(q11q13) - hypogonad - hypotonia - mental retardation - behavior probs - uncrontrolled appetite






47. Metastatic stomach CA to ovary






48. Tumor suppressor mutated in Von Recklinhousen






49. Aneurysm at small artery bifurcations






50. Polyostotic fibrous dysplasia - precocious puberty - caf